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DeCS
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Descriptor English:
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Isovaleryl-CoA Dehydrogenase
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Descriptor Spanish:
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Isovaleril-CoA Deshidrogenasa
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Descriptor Portuguese:
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Isovaleril-CoA Desidrogenase
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Tree Number:
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D08.811.682.660.462
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Definition Spanish:
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Flavoproteína mitocondrial que cataliza la oxidación del 3-metilbutanoil-CoA a 3-metilbut-2-enoil-CoA usando FAD como cofactor. Los defectos de esta enzima se asocian a acidemia isovalérica (AIV).
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Allowable Qualifiers Spanish:
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Record Number:
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50628
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Unique Identifier:
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D050769
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Occurrence in VHL:
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Similar:
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DeCS CID-10 SciELO LILACS LIS
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